Brain cavernomas associated with en coup de sabre linear scleroderma: Two case reports
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چکیده
منابع مشابه
Brain cavernomas associated with en coup de sabre linear scleroderma: Two case reports
Linear scleroderma is a form of localized scleroderma that primarily affects the pediatric population. When it occurs on the scalp or forehead, it is termed "en coup de sabre". In the en coup de sabre subtype, many extracutaneous associations, mostly neurological, have been described. A patient with linear scleroderma en coup de sabre was noted to have ipsilateral brain cavernomas by magnetic r...
متن کاملLinear scleroderma en coup de sabre with associated neurologic abnormalities.
Linear scleroderma represents a unique form of localized scleroderma that primarily affects the pediatric population, with 67% of patients diagnosed before 18 years of age. When linear scleroderma occurs on the head, it is referred to as linear scleroderma en coup de sabre, given the resemblance of the skin lesions to the stroke of a sabre. Here we describe 3 pediatric patients with linear scle...
متن کاملScleroderma en coup de sabre.
A case of scleroderma 'en coup de sabre' presenting with uveitis, predominantly posterior, and intractable grand mal seizures is described. The histopathology specimens and neuroradiology investigations reaffirm the clinical impression that inflammation is not solely confined to the skin in this form of linear scleroderma.
متن کاملAtypical Neuroimaging Manifestations of Linear Scleroderma “en coup de sabre”
Linear scleroderma "en coup de sabre" is a subset of localized scleroderma with band-like sclerotic lesions typically involving the fronto-parietal regions of the scalp. Patients often present with neurologic symptoms. On imaging, patients may have lesions in the cerebrum ipsilateral to the scalp abnormality. Infratentorial lesions and other lesions not closely associated with the overlying sca...
متن کاملA familial case of scleroderma en coup de sabre.
Sir, Linear scleroderma represents a rare disease, more often observed in the pediatric age group. The lower extremities are usually involved; less commonly it affects the frontoparietal area and the anterior scalp. Recently, a large case series of frontoparietal scleroderma en coup de sabre has been reported (1), but in this series, as well as in the English language literature, to the best of...
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ژورنال
عنوان ژورنال: Pediatric Rheumatology
سال: 2011
ISSN: 1546-0096
DOI: 10.1186/1546-0096-9-18